Abstract: Abernethy malformation is an abnormal extrahepatic portosystemic venous shunt vascular
malformation which is relatively rare and has a variety of clinical manifestations. It can manifest as portal
hypertension, multiple nodules of the liver and gastrointestinial bleeding. Abdominal ultrasonography
is helpful for early screening of Abernethy malformation. CT angiography (CTA), magnetic resonance
angiography (MRA) and digital subtraction angiography (DSA) can be used as the best diagnosis and typing
of Abernethy malformation. In this paper, a case of Abernethy malformation firstly diagnosed as liver cirrhosis
in our hospital was reported and the involved literatures were reviewed and analyzed.